Imaging in portal cavernoma cholangiopathy: current understanding and future perspectives

Portal cavernoma cholangiopathy (PCC) as the name suggests refers to the spectrum of biliary changes that occur secondary to cavernomatous transformation of the portal vein in patients with extrahepatic portal vein obstruction (EHPVO) (1-5). PCC has previously been widely referred to as ‘portal biliopathy’ in medical literature but the current terminology is perhaps more readily comprehensible.